Tumor-Like Primary Central Nervous System Vasculitis With Spina Involvement:Report of One Case

Li ZHANG, Hui SUN, Shimin ZHANG, Sai GAO, Lei WU, Dehui HUANG

Acta Academiae Medicinae Sinicae ›› 2024, Vol. 46 ›› Issue (3) : 466-470.

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Acta Academiae Medicinae Sinicae

Abbreviation (ISO4): Acta Academiae Medicinae Sinicae      Editor in chief: Xuetao CAO

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Acta Academiae Medicinae Sinicae ›› 2024, Vol. 46 ›› Issue (3) : 466-470. DOI: 10.3881/j.issn.1000-503X.15762
Case Reports

Tumor-Like Primary Central Nervous System Vasculitis With Spina Involvement:Report of One Case

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Abstract

Primary central nervous system vasculitis(PACNS)is a vasculitic disorder affecting small to medium-sized blood vessels primarily in the central nervous system,involving the brain,spinal cord,and meninges.tumor-like PNCAS,a rare subtype of PACNS,is often misdiagnosed as intracranial malignancy,and that with spinal cord involvement is even more uncommon.the lack of specific clinical symptoms and imaging manifestations poses a challenge to the diagnosis of PACNS.this report presents a case of Tumor-like PACNS with spinal cord involvement based on the pathological evidence,aiming to enrich the knowledge about This condition。

Key words

primary central nervous system vasculitis / spinal cord involvement / electromyography

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Li ZHANG , Hui SUN , Shimin ZHANG , et al . Tumor-Like Primary Central Nervous System Vasculitis With Spina Involvement:Report of One Case[J]. Acta Academiae Medicinae Sinicae. 2024, 46(3): 466-470 https://doi.org/10.3881/j.issn.1000-503X.15762

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